Ventriculoarterial Malconnections
Anomalies of ventriculoarterial connection includes those lesions associated with
abnormal connection between the ventricular mass and the great arteries. Lesions in this
category include truncus arteriosus, tetralogy of Fallot, double outlet ventricles, and
transposition of the great vessels.
To understand the morphology of ventriculoarterial malconnections, it is important to
first understand the anatomy of the normal
ventriculoarterial connection, which is dealt with separately.
A classification of ventriculoarterial malconnections includes:
- Truncus Arteriosus
- Tetralogy of Fallot
- Tetralogy of Fallot and Pulmonary Stenosis
Tetralogy of Fallot and Pulmonary Atresia
Tetralogy of Fallot and Pulmonary Insufficiency
- Double Outlet Right Ventricle
- Transposition of the Great Arteries
- d-Transposition of the Great Arteries
l-Transposition of the Great Arteries
A summary of the morphologic features of ventriculoarterial malconnections is
included in the following table:
Comparison of morphologic features of the major ventriculoarterial
malconnections
| |
Truncus Arteriosus |
Tetralogy of Fallot |
DORV |
d-TGA |
| Subaortic conus |
-- |
-- |
++ / - |
++ |
| Subpulmonary conus |
NA |
++ |
+ / - |
-- |
| TC-PV distance |
distant |
distant |
highly variable |
fibrous continuity |
| AV-MV distance |
fibrous continuity |
fibrous continuity |
highly variable |
distant |
| LVOTO |
+/- |
rare |
+/- |
not uncommon |
| RVOTO |
+/- |
yes |
+/- |
rare |
| VSD |
subaortic |
subaortic |
variable |
subpulmonary |
|